Abstract
Eisenmenger's syndrome is characterized by a right-to-left or bidirectional shunt
in congenital heart diseases. Hemolysis, elevated liver enzymes and low platelet count
(HELLP) syndrome, commonly occurring during pregnancy, includes hemolysis, elevated
liver enzymes and low platelet counts. HELLP syndrome and pregnancy are extremely
rare in patients with Eisenmenger's syndrome. The authors report 4 cases of pregnancy
complicated by the HELLP and Eisenmenger's syndrome and describe their initial intervention
and the in-hospital outcomes of these cases. Special emphasis is given to elaborate
about the hemodynamic monitoring, magnesium sulphate for convulsions, corticosteroid
treatment, anticoagulation therapy, management of pulmonary hypertension, the timing
of delivery, and blood product transfusion.
Key Indexing Terms
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Article info
Publication history
Accepted:
November 6,
2012
Received:
July 13,
2012
Footnotes
The authors have no financial or other conflicts of interest to disclose.
Identification
Copyright
© 2013 Southern Society for Clinical Investigation. Published by Elsevier Inc. All rights reserved.
